Aggressive desmoid fibromatosis : first case in a Rwandan child

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dc.contributor.authorKanyamuhunga, Aimableen_ZA
dc.contributor.authorMcCall, Natalieen_ZA
dc.contributor.authorTuyisenge, Lisinee
dc.contributor.authorMumena, Crispusen_ZA
dc.contributor.authorStefan, Daniela Cristinaen_ZA
dc.date.accessioned2014-07-07T12:33:23Z
dc.date.available2014-07-07T12:33:23Z
dc.date.issued2013-08-30
dc.descriptionCITATION: Kanyamuhunga, A. et al. 2013. Aggressive desmoid fibromatosis : first case in a Rwandan child. South African Journal of Child Health, 7(3):117-118, doi:10.7196/SAJCH.593.
dc.descriptionThe original publication is available at http://www.sajch.org.za
dc.description.abstractDesmoid tumours are a rare group of locally aggressive, non-malignant tumours of fibroblastic origin that can result in significant morbidity due to local invasion. Facial involvement in children with aggressive fibromatosis is uncommon. We present the case of a 14-month-old Rwandan child with an aggressive desmoid tumour involving the left mid-facial region. The patient presented with severe stertor due to massive nasal obstruction. After intensive supportive care the diagnosis was confirmed histopathologically. Treatment consisted of eight courses of chemotherapy with vincristine, actinomycin-D and cyclophosphamide followed by surgical removal of the remaining mass. The outcome was impressive and encouraging.
dc.description.urihttp://www.sajch.org.za/index.php/SAJCH/article/view/593
dc.description.versionPublisher's version
dc.format.extent3 pages
dc.identifier.citationKanyamuhunga, A. et al. 2013. Aggressive desmoid fibromatosis : first case in a Rwandan child. South African Journal of Child Health, 7(3):117-118, doi:10.7196/SAJCH.593.
dc.identifier.issn1999-7671 (online)
dc.identifier.issn1994-3032 (print)
dc.identifier.otherdoi:10.7196/SAJCH.593
dc.identifier.urihttp://hdl.handle.net/10019.1/94812
dc.language.isoen
dc.publisherHealth & Medical Publishing Group
dc.rights.holderAuthors retain copyright
dc.subjectFibromatosisen_ZA
dc.subjectDesmoid tumoursen_ZA
dc.titleAggressive desmoid fibromatosis : first case in a Rwandan childen_ZA
dc.typeArticle
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