Progressive familial heart block type I : clinical and pathological observations

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dc.contributor.authorVan der Merwe, P.-L.en_ZA
dc.contributor.authorRose, A. G.en_ZA
dc.contributor.authorVan der Walt, J. J.en_ZA
dc.contributor.authorWeymar, H. W.en_ZA
dc.contributor.authorHunter, J. C.en_ZA
dc.contributor.authorWeich, H. F. H.en_ZA
dc.date.accessioned2011-03-18T14:57:17Z
dc.date.available2011-03-18T14:57:17Z
dc.date.issued1991
dc.descriptionCITATION: 1991: .Van der Merwe, P.-L. et al. 1991. Progressive familial heart block type I : clinical and pathological observations. South African Medical Journal, 80:34-38.
dc.descriptionThe original publication is available at http://www.samj.org.za
dc.description.abstractProgressive familial heart block type I (PFHB-I) is an autosomal inherited disease. It was previously postulated that the disease is limited to the cardiac conduction tissue. The presentation of a patient with dilated cardiomyopathy focused on the possibility that this might be part of PFHB-I. This observation led to routine echocardiographic examination of patients with complete heart block, who belonged to PFHB-I families, and another 5 cases with signs of dilated cardiomyopathy were identified. This is the first time, to our knowledge, that the histological picture of PFHB-I has been described. From these case reports it is clear that in the presence of a dilated cardiomyopathy the prognosis in PFHB-I tends to be poor.
dc.description.versionPublisher’s version
dc.format.extent5 pages
dc.identifier.issn2078-5135 (online)
dc.identifier.issn0256-9574 (print)
dc.identifier.urihttp://hdl.handle.net/10019.1/7318
dc.language.isoen
dc.publisherHealth & Medical Publishing Group
dc.rights.holderSouth African Medical Journal
dc.subjectHeart -- Abnormalitiesen_ZA
dc.titleProgressive familial heart block type I : clinical and pathological observationsen_ZA
dc.typeArticle
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