Systemic juvenile xanthogranulomatosis imitating a malignant abdominal wall tumor with lung metastases
Date
2007
Authors
Matcham N.J.
Andronikou S.
Sibson K.
Ramani P.
Grier D.
Journal Title
Journal ISSN
Volume Title
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Abstract
Juvenile xanthogranulomatosis (JXG) is a rare benign condition, which usually presents with characteristic skin lesions and can be diagnosed clinically. However, systemic JXG may involve a wide range of extracutaneous sites and may pose a diagnostic dilemma for the clinician, radiologist, and pathologist. In particular it may simulate malignancy. Here, we report a case of systemic JXG within the abdominal wall musculature and lungs, which imitated a sarcoma with pulmonary metastases on computerized tomography. To the best of our knowledge, this is the first such reported case. In particular, systemic disease presenting without skin lesions is unusual. © 2007 Lippincott Williams & Wilkins, Inc.
Description
Keywords
cytarabine, daunorubicin, etoposide, prednisolone, abdominal tumor, abdominal wall musculature, abdominal wall tumor, benign tumor, cancer combination chemotherapy, cancer surgery, case report, computer assisted tomography, conference paper, female, human, human tissue, juvenile xanthogranuloma, lung metastasis, preschool child, priority journal, systemic disease, tumor biopsy, tumor localization, tumor recurrence, Abdominal neoplasms, Abdominal wall, Child, Preschool, False positive reactions, Female, Humans, Lung Neoplasms, Neoplasm metastasis, Sarcoma, Tomography Scanners, X-Ray Computed, Xanthogranuloma, Juvenile
Citation
Journal of Pediatric Hematology/Oncology
29
1
29
1