Browsing by Author "Van der Merwe, P.-L."
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- ItemKawasaki disease masquerading as anomalous origin of left coronary artery from the pulmonary artery(Health & Medical Publishing Group, 1999) Waggie, Z.; Van der Merwe, P.-L.; Kalis, N. N.Although myocardial ischaemia/infarction is rare in childhood, it is a well-described complication of both Kawasaki disease (KD) and anomalous origin of the left coronary artery from the pulmonary artery (AOLCA). We describe a case of Kawasaki disease appearing as an AOLCA in a 2-year-old boy with myocardial infarction.
- ItemProgressive familial heart block (type I) : a follow-up study after 10 years(Health & Medical Publishing Group, 1988) Van der Merwe, P.-L.; Weymar, H. W.; Torrington, M.; Brink, A. J.A follow-up study was done on 55 patients, all members of families with type I progressive familial heart block (PFHB) examined during 1977. Of the 55 patients 5 had died, 17 had normal ECGs while 7 with previously abnormal ECGs remained unchanged. All the others had progressed to a more severe form of heart block and 8 of them had received permanent pacemakers. These findings again emphasise the importance of regular ECG follow-up examinations of members of PFHB families.
- ItemProgressive familial heart block type I : clinical and pathological observations(Health & Medical Publishing Group, 1991) Van der Merwe, P.-L.; Rose, A. G.; Van der Walt, J. J.; Weymar, H. W.; Hunter, J. C.; Weich, H. F. H.Progressive familial heart block type I (PFHB-I) is an autosomal inherited disease. It was previously postulated that the disease is limited to the cardiac conduction tissue. The presentation of a patient with dilated cardiomyopathy focused on the possibility that this might be part of PFHB-I. This observation led to routine echocardiographic examination of patients with complete heart block, who belonged to PFHB-I families, and another 5 cases with signs of dilated cardiomyopathy were identified. This is the first time, to our knowledge, that the histological picture of PFHB-I has been described. From these case reports it is clear that in the presence of a dilated cardiomyopathy the prognosis in PFHB-I tends to be poor.
- ItemProgressive familial heart block: Part I. Extent of the disease(Health & Medical Publishing Group, 1986-09) Torrington, Marie; Weymar, H. W.; Van der Merwe, P.-L.; Brink, A. J.ENGLISH ABSTRACT: Progressive familial heart block (type I) has been identified in the RSA. Since 1977 many families have been referred for pedigree tracing. The present probands of some 9 pedigrees are the descendants of specific children of an immigrant; other genetic diseases appear in these pedigrees. The necessity of identifying, diagnosing and possibly treating the descendants of carriers is emphasized.