Systemic juvenile xanthogranulomatosis imitating a malignant abdominal wall tumor with lung metastases
dc.contributor.author | Matcham N.J. | |
dc.contributor.author | Andronikou S. | |
dc.contributor.author | Sibson K. | |
dc.contributor.author | Ramani P. | |
dc.contributor.author | Grier D. | |
dc.date.accessioned | 2011-05-15T16:17:07Z | |
dc.date.available | 2011-05-15T16:17:07Z | |
dc.date.issued | 2007 | |
dc.description.abstract | Juvenile xanthogranulomatosis (JXG) is a rare benign condition, which usually presents with characteristic skin lesions and can be diagnosed clinically. However, systemic JXG may involve a wide range of extracutaneous sites and may pose a diagnostic dilemma for the clinician, radiologist, and pathologist. In particular it may simulate malignancy. Here, we report a case of systemic JXG within the abdominal wall musculature and lungs, which imitated a sarcoma with pulmonary metastases on computerized tomography. To the best of our knowledge, this is the first such reported case. In particular, systemic disease presenting without skin lesions is unusual. © 2007 Lippincott Williams & Wilkins, Inc. | |
dc.description.version | Conference Paper | |
dc.identifier.citation | Journal of Pediatric Hematology/Oncology | |
dc.identifier.citation | 29 | |
dc.identifier.citation | 1 | |
dc.identifier.issn | 10774114 | |
dc.identifier.other | 10.1097/MPH.0b013e318030ac5e | |
dc.identifier.uri | http://hdl.handle.net/10019.1/14081 | |
dc.subject | cytarabine | |
dc.subject | daunorubicin | |
dc.subject | etoposide | |
dc.subject | prednisolone | |
dc.subject | abdominal tumor | |
dc.subject | abdominal wall musculature | |
dc.subject | abdominal wall tumor | |
dc.subject | benign tumor | |
dc.subject | cancer combination chemotherapy | |
dc.subject | cancer surgery | |
dc.subject | case report | |
dc.subject | computer assisted tomography | |
dc.subject | conference paper | |
dc.subject | female | |
dc.subject | human | |
dc.subject | human tissue | |
dc.subject | juvenile xanthogranuloma | |
dc.subject | lung metastasis | |
dc.subject | preschool child | |
dc.subject | priority journal | |
dc.subject | systemic disease | |
dc.subject | tumor biopsy | |
dc.subject | tumor localization | |
dc.subject | tumor recurrence | |
dc.subject | Abdominal neoplasms | |
dc.subject | Abdominal wall | |
dc.subject | Child, Preschool | |
dc.subject | False positive reactions | |
dc.subject | Female | |
dc.subject | Humans | |
dc.subject | Lung Neoplasms | |
dc.subject | Neoplasm metastasis | |
dc.subject | Sarcoma | |
dc.subject | Tomography Scanners, X-Ray Computed | |
dc.subject | Xanthogranuloma, Juvenile | |
dc.title | Systemic juvenile xanthogranulomatosis imitating a malignant abdominal wall tumor with lung metastases | |
dc.type | Conference Paper |