Systemic juvenile xanthogranulomatosis imitating a malignant abdominal wall tumor with lung metastases

dc.contributor.authorMatcham N.J.
dc.contributor.authorAndronikou S.
dc.contributor.authorSibson K.
dc.contributor.authorRamani P.
dc.contributor.authorGrier D.
dc.date.accessioned2011-05-15T16:17:07Z
dc.date.available2011-05-15T16:17:07Z
dc.date.issued2007
dc.description.abstractJuvenile xanthogranulomatosis (JXG) is a rare benign condition, which usually presents with characteristic skin lesions and can be diagnosed clinically. However, systemic JXG may involve a wide range of extracutaneous sites and may pose a diagnostic dilemma for the clinician, radiologist, and pathologist. In particular it may simulate malignancy. Here, we report a case of systemic JXG within the abdominal wall musculature and lungs, which imitated a sarcoma with pulmonary metastases on computerized tomography. To the best of our knowledge, this is the first such reported case. In particular, systemic disease presenting without skin lesions is unusual. © 2007 Lippincott Williams & Wilkins, Inc.
dc.description.versionConference Paper
dc.identifier.citationJournal of Pediatric Hematology/Oncology
dc.identifier.citation29
dc.identifier.citation1
dc.identifier.issn10774114
dc.identifier.other10.1097/MPH.0b013e318030ac5e
dc.identifier.urihttp://hdl.handle.net/10019.1/14081
dc.subjectcytarabine
dc.subjectdaunorubicin
dc.subjectetoposide
dc.subjectprednisolone
dc.subjectabdominal tumor
dc.subjectabdominal wall musculature
dc.subjectabdominal wall tumor
dc.subjectbenign tumor
dc.subjectcancer combination chemotherapy
dc.subjectcancer surgery
dc.subjectcase report
dc.subjectcomputer assisted tomography
dc.subjectconference paper
dc.subjectfemale
dc.subjecthuman
dc.subjecthuman tissue
dc.subjectjuvenile xanthogranuloma
dc.subjectlung metastasis
dc.subjectpreschool child
dc.subjectpriority journal
dc.subjectsystemic disease
dc.subjecttumor biopsy
dc.subjecttumor localization
dc.subjecttumor recurrence
dc.subjectAbdominal neoplasms
dc.subjectAbdominal wall
dc.subjectChild, Preschool
dc.subjectFalse positive reactions
dc.subjectFemale
dc.subjectHumans
dc.subjectLung Neoplasms
dc.subjectNeoplasm metastasis
dc.subjectSarcoma
dc.subjectTomography Scanners, X-Ray Computed
dc.subjectXanthogranuloma, Juvenile
dc.titleSystemic juvenile xanthogranulomatosis imitating a malignant abdominal wall tumor with lung metastases
dc.typeConference Paper
Files