Tricuspid atresia - Profile and outcome

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dc.contributor.authorKeating P.
dc.contributor.authorVan der Merwe P.-L.
dc.contributor.authorShipton S.
dc.date.accessioned2011-05-15T16:15:55Z
dc.date.available2011-05-15T16:15:55Z
dc.date.issued2001
dc.description.abstractTricuspid atresia (TA) is the third most common cyanotic congenital cardiac lesion, with a mortality rate of 90% before the age of 10 years. Surgical intervention has reduced the mortality, but with unfavourable anatomy the mortality remains high. The aim of this study was to look at the profile of a cohort of children with TA and to evaluate treatment modalities and outcome. Twenty-seven children were included in this retrospective descriptive study. Twenty-three were referred with central cyanosis and 25% with cardiac failure. All patients had a left superior QRS axis on electrocardiogram (ECG). Eleven patients died, 8 before surgical intervention and 3 postoperatively. Outcome was mainly influenced by the anatomy of the pulmonary arteries especially when the pulmonary arteries were extremely hypoplastic. Patients with increased pulmonary blood flow did better than those with decreased pulmonary blood flow. There was a statistically significant difference in survival between the surgical and non-surgical groups. Few of our patients qualified for the Fontan procedure mainly because of increased pulmonary pressures in the high pulmonary blood flow group and severe hypoplastic pulmonary arteries in the low pulmonary blood flow group. Early referral is essential for palliation so that more definitive surgery can be done to achieve better results.
dc.description.versionArticle
dc.identifier.citationCardiovascular Journal of South Africa
dc.identifier.citation12
dc.identifier.citation4
dc.identifier.issn10159657
dc.identifier.urihttp://hdl.handle.net/10019.1/13546
dc.subjectartery dysplasia
dc.subjectarticle
dc.subjectchild
dc.subjectclinical article
dc.subjectcyanosis
dc.subjectfemale
dc.subjectheart failure
dc.subjecthuman
dc.subjectinfant
dc.subjectlung blood flow
dc.subjectlung pressure
dc.subjectmale
dc.subjectpatient referral
dc.subjectQRS complex
dc.subjecttricuspid valve atresia
dc.subjectChild, Preschool
dc.subjectFemale
dc.subjectFontan Procedure
dc.subjectHumans
dc.subjectInfant
dc.subjectInfant, Newborn
dc.subjectMale
dc.subjectPostoperative Complications
dc.subjectProstaglandins
dc.subjectRetrospective Studies
dc.subjectTreatment Outcome
dc.subjectTricuspid Atresia
dc.titleTricuspid atresia - Profile and outcome
dc.typeArticle
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